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Эхокардиографическое обследование по стандартной методике было проведено 55 детям с некомпактным миокардом. Диагноз “некомпактный миокард” устанавливался на основании ультразвуковых критериев, разработанных Chin T.K. et al. (1990) и Jenni R. et al. (2007). У 9 из 55 обследованных пациентов были выявлены аневризмы левого желудочка. Аневризмы локализовались в области апикальноперегородочного, апикальнобокового и среднебокового сегментов. Во всех случаях в области аневризм определялось более выраженное нарушение сократимости миокарда, чем в остальных его участках. Полость аневризмы, а также сообщение с полостью левого желудочка визуализировались как в момент диастолы, так и в момент систолы желудочка. У одного пациента в области аневризмы был выявлен тромб. Аневризмы левого желудочка являются нередким осложнением некомпактного миокарда у детей (16%). При выявлении аневризм левого желудочка у детей в диагностический поиск должен быть включен диагноз “некомпактный миокард”.
Ключевые слова:
эхокардиография, не компактный миокард, аневризмы левого желудочка, дети.
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55 children with noncompaction of myocardium underwent standard echocardiography. Diagnosis of myocardial noncompaction was done according to the ultrasound criteria which were developed by Chin T.K. et al. (1990) and Jenni R. et al. (2007). Left ventricular aneurysms were revealed in 9 of 55 patients. They localized in apical septal, apical lateral, and mid lateral segments. In all cases more significant disorders of myocardium contractility were detected in aneurysm location. Aneurysm and its connection with left ventricle visualized at ventricle diastole and ventricle systole as well. Thrombus in aneurysm was revealed in one patient. Left ventricle aneurysm is the frequent complication of myocardial noncompaction in children (16%). Diagnosis of myocardial noncompaction should be included in diagnostic algorithm in children with left ventricle aneurysms.
Keywords:
echocardiography, noncompaction of myocardium, left ventricular aneurysms, and children.